The porphyrin compound in human body mainly includes hemoglobin, protoheme, protoporphyrin, coproporphyrin, uro-porphyrin and so on.
人体中含有的卟啉化有血红蛋白、血红素、原卟啉、粪卟啉、尿卟啉等。
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Protoporphyrinogen IX is converted to protoporphyrin IX by protoporphyrinogen oxidase.
原卟原IX在原卟原氧催下生成原卟IX。
Protoporphyrinogen IX is converted a protoporphyrin IX by protoporphyrinogen oxidase.
原卟原IX原卟原氧为原卟IX。
Lastly, an iron molecule is added to a protoporphyrin IX via the enzyme ferrochelatase.
最后,铁分子通过亚铁螯合添加到原卟IX中。
Now with sideroblastic anemia, there's defective protoporphyrin synthesis, which results in impaired incorporation of iron to form heme.
在铁粒幼细胞性贫中,原卟合成存在缺陷,导致铁结合形成红素的能力受损。
Lastly, an iron molecule is added to protoporphyrin IX via the enzyme ferrochelatase, and viola! We got ourselves a completed heme!
最后,一个铁分子在亚铁螯合作用下加在原卟IX上;你看!我们得到了一个完整的红素!
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