mutase

Prosthetic enzyme of mutase, catalyze reactions of group, mainly methyl, metachoresis in the interior of substrate molecule.

变位的辅，催化底物分子内基团(主要为甲基)的变位反应。

Methylmalonic acidemia is an inherited metabolic disorder,which is caused by deficiency of methylmalonyl-coenzyme A mutase or its cofactor adenosylcobalamin.

甲基丙二酸血症是由于甲基丙二辅A变位或其辅腺苷钴胺素缺陷所致的一种遗传性代谢疾病。